Chemotherapy is a chemical cocktail intravenously fed to the body to target cancer cells and kill them. Optic nerve glioma with complete intraocular extension ncbi. A relationship between optic nerve glioma and nf1 is well established. Optic glioma definition of optic glioma by medical. This worksheet is in pdf format and holds a printable version of the quiz optic chiasma and cranial nerve iii. Gliomas of the optic pathways that occur in adults are rare tumours. This is a single case and should be interpreted with caution. In this setting, the tumors are often lowgrade and indolent.
Optic nerve, chiasmal, and hypothalamic tumors society for. Gliomas isolated to the optic nerve ong represent a subgroup of optic pathway gliomas, and their treatment remains controversial. In most series, the 5year eventfree survival is in the. By printig out this quiz and taking it with pen and paper creates for a good variation to only playing it online. Any surgical maneuver within the subarachnoid space puts the optic nerve at risk. However, externalbeam radiation therapy has been associated with good visual outcomes and tumorfree progression rates in other series. Pdf summary optic pathway gliomas account for 35% of all pediatric cns tumors and represent the. Primary tumours of the optic nerve and its sheath eye. Gliomas are the most common type of primary central nervous system cns tumor in children, making up approximately 50% of all pediatric brain and cns tumors 1,2 with an overall population incidence rate of 34 per 100,000. Males and females are approximately equally affected. Optic nerve sheath decompression has been reported to be beneficial in treating optic nerve glioma, although in our patient there was no appreciable egress of csf when the optic nerve sheath was opened.
Optic nerve gliomas comprise about 1% of all intracranial tumors. Optic nerve glioma and the management british journal of. Optic nerve gliomas account for 1%5% of all intracranial. We suggest a method ofmanagement ofprimary optic nerve tumours, both meningiomas and gliomas, in young. Orbital optic nerve glioma in adult life jama network. An optic nerve glioma is a rare type of brain tumor found in the optic chiasm, where the optic nerves cross. Optic glioma warranting treatment in children nature. Symptoms may include loss of vision, secondary strabismus, exophthalmos, and ocular paralysis. Optic pathway gliomas in children american academy of. The treatment of optic nerve gliomas has changed considerably over the past few years.
Optic pathway gliomas typically present in children, accounting for 1015% of supratentorial tumors in this age group, and are often in the setting of neurofibromatosis type 1 nf1 1063% 3. While nf1associated gliomas can be found in several brain regions, the majority arise in the optic nerves, chiasm, tracks, and radiations optic. About 10% of optic pathway tumors are located within an optic nerve. Computed tomography and magnetic resonance imaging mri of brainorbit showed a fusiform enlargement of the left optic nerve and total. Optic nerve glioma is the most common optic nerve tumour.
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